Summary
We report a patient with paradoxical vocal fold motion (PVFM) due to pantothenate
kinase-associated neurodegeneration, a rare neurodegenerative disease and a subclass
of neurodegeneration with brain iron accumulation disorders. PVFM is marked by normal
vocal fold anatomy and physiology with intermittent adduction during the respiratory
cycle. Many etiologies have been reported and include laryngeal hypersensitivity such
as asthma and gastroesophageal reflux, functional disorders, and neurologic disorders
such as focal respiratory dystonia. This case highlights the occasional association
of PVFM with underlying neurologic disorders, especially those that disrupt autonomic
functioning.
Key Words
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Article info
Publication history
Published online: July 29, 2013
Accepted:
April 19,
2013
Identification
Copyright
© 2013 The Voice Foundation. Published by Elsevier Inc. All rights reserved.
